Overview

Variant ID 1456
Entrez Gene ID 2475
Gene MTOR (GeneCards)
Location hg19 1:11188164-11188164
hg38 1:11128107-11128107
Disease Focal Cortical Dysplasias (view all the variants in this disease)
Method Sanger
Mutation(HGVS format) NC_000001.10:g.11188164 G>C (Genome Assembly: hg19)

Other information

Exon or Intron NA
Position in protein 1977
Amino acid changes in protein T > R
Position in cDNA NA
Changes in cDNA NA > NA
mRNA accession NM_004958.3
mRNA length 8733
Reference length 249250621

Annotations and predictions

MAF in gnomAD genome (version 2.0.1) 0
Variant IDs in COSMIC (version 89) 462602
Variant occurences in COSMIC 1(haematopoietic_and_lymphoid_tissue)|1(prostate)|2(kidney)|2(large_intestine)
EIGEN score 0.9794
CADD Raw score (version 1.3) 6.704108 (Deleterious)
FATHMM raw prediction score 0.99401 (Tolerated)
SIFT score 0 (Deleterious)
LRT score 0 (Deleterious)
MutationTaster score 1 (Deleterious)
MutatioinAssessor score 3.295 (Deleterious)
PROVEAN score -5.17 (Deleterious)
MetaSVM score 0.591 (Deleterious)
MetaLR score 0.733 (Deleterious)
MCAP score 0.143 (Deleterious)
FitCons score 0.707 (Highly Significant p < 0.003 )
Genomic Evolutionary Rate Profiling (GERP) score 5.8
PhyloP score based on multiple alignment of 100 vertebrates 9.317
PhastCons score based on multiple alignment of 100 vertebrates 1
SiPhy log transformed odds ratio on multiple alignment of 29 mammals 20.063
Deleterious probability by iFish2 0.9953 (Deleterious)
Deleterious probability by DeFine 0.9183 (Deleterious)
Entrez Gene ID 2475 (NCBI Gene)
Official Gene Symbol MTOR (GeneCards)
Number of variants in MTOR in this database 21 (view all the variants)
Full name mechanistic target of rapamycin kinase
Band 1p36.22
Other IDs Vega: OTTHUMG00000002001
OMIM: 601231
HGNC: HGNC:3942
Ensembl: ENSG00000198793
Other names SKS, FRAP, FRAP1, FRAP2, RAFT1, RAPT1
Summary The protein encoded by this gene belongs to a family of phosphatidylinositol kinase-related kinases. These kinases mediate cellular responses to stresses such as DNA damage and nutrient deprivation. This protein acts as the target for the cell-cycle arrest and immunosuppressive effects of the FKBP12-rapamycin complex. The ANGPTL7 gene is located in an intron of this gene. [provided by RefSeq, Sep 2008]

Individual #1

Individual ID 29281825.05 (view all the variants in this individual)
Pubmed ID 29281825
Whose mosaic mutation Female Patient  
Phenotype 3  
Disease Focal Cortical Dysplasias (view all the variants in this disease)
OMIM ID 607341

Publication #1: 29281825

Pubmed ID 29281825
Title Somatic Mutations Activating the mTOR Pathway in Dorsal Telencephalic Progenitors Cause a Continuum of Cortical Dysplasias.
Journal Cell Reports
Publication date 2017.12
Disease Hemimegalencephaly;Focal Cortical Dysplasias
Number of cases Male cases: 7; Female cases: 7;