Overview

Variant ID 29681
Entrez Gene ID 5582
Gene PRKCG (GeneCards)
Location hg19 19:54395806-54395806
hg38 19:53892552-53892552
Disease Autism Spectrum Disorders (view all the variants in this disease)
Method MiSeq
Mutation(HGVS format) NC_000019.9:g.54395806 G>T (Genome Assembly: hg19)

Other information

Exon or Intron NA
Position in protein NA
Amino acid changes in protein NA > NA
Position in cDNA NA
Changes in cDNA NA > NA
mRNA accession NA
mRNA length NA
Reference length 59128983

Annotations and predictions

MAF in gnomAD genome (version 2.0.1) 0
EIGEN score -0.087
CADD Raw score (version 1.3) 3.943018 (Deleterious)
FATHMM raw prediction score 0.95079 (Tolerated)
SIFT score 0.06 (Tolerated)
MutationTaster score 1 (Deleterious)
MutatioinAssessor score 1.75 (Tolerated)
PROVEAN score -2.33 (Tolerated)
MetaSVM score -0.758 (Tolerated)
MetaLR score 0.203 (Tolerated)
MCAP score 0.043 (Deleterious)
FitCons score 0.706 (Highly Significant p < 0.003 )
Genomic Evolutionary Rate Profiling (GERP) score 3.2
PhyloP score based on multiple alignment of 100 vertebrates 3.106
PhastCons score based on multiple alignment of 100 vertebrates 1
SiPhy log transformed odds ratio on multiple alignment of 29 mammals 9.912
Deleterious probability by iFish2 0.5091 (Deleterious)
Deleterious probability by DeFine 0.9018 (Deleterious)
Entrez Gene ID 5582 (NCBI Gene)
Official Gene Symbol PRKCG (GeneCards)
Number of variants in PRKCG in this database 1 (view all the variants)
Full name protein kinase C gamma
Band 19q13.42
Other IDs Vega: OTTHUMG00000064846
OMIM: 176980
HGNC: HGNC:9402
Ensembl: ENSG00000126583
Other names PKCC, PKCG, SCA14, PKC-gamma
Summary Protein kinase C (PKC) is a family of serine- and threonine-specific protein kinases that can be activated by calcium and second messenger diacylglycerol. PKC family members phosphorylate a wide variety of protein targets and are known to be involved in diverse cellular signaling pathways. PKC also serve as major receptors for phorbol esters, a class of tumor promoters. Each member of the PKC family has a specific expression profile and is believed to play distinct roles in cells. The protein encoded by this gene is one of the PKC family members. This protein kinase is expressed solely in the brain and spinal cord and its localization is restricted to neurons. It has been demonstrated that several neuronal functions, including long term potentiation (LTP) and long term depression (LTD), specifically require this kinase. Knockout studies in mice also suggest that this kinase may be involved in neuropathic pain development. Defects in this protein have been associated with neurodegenerative disorder spinocerebellar ataxia-14 (SCA14). Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Oct 2015]

Individual #1

Individual ID 28714951.357 (view all the variants in this individual)
Pubmed ID 28714951
Whose mosaic mutation Patient  
Phenotype 3  
Disease Autism Spectrum Disorders (view all the variants in this disease)
OMIM ID 209850

Publication #1: 28714951

Pubmed ID 28714951
Title Rates, distribution and implications of postzygotic mosaic mutations in autism spectrum disorder
Journal Nat Neurosci
Publication date 2017.07
Disease Autism Spectrum Disorders
Incidence 0.01
Number of cases cases of unknown sex: 376;