Overview

Variant ID 29729
Entrez Gene ID 8647
Gene ABCB11 (GeneCards)
Location hg19 2:169853212-169853212
hg38 2:168996702-168996702
Disease Autism Spectrum Disorders (view all the variants in this disease)
Method NextSeq500
Mutation(HGVS format) NC_000002.11:g.169853212 T>G (Genome Assembly: hg19)

Other information

Exon or Intron Exon
Position in protein NA
Amino acid changes in protein NA > NA
Position in cDNA NA
Changes in cDNA NA > NA
mRNA accession NA
mRNA length NA
Reference length 243199373

Annotations and predictions

MAF in gnomAD genome (version 2.0.1) 0
EIGEN score 0.4198
CADD Raw score (version 1.3) 4.091438 (Deleterious)
FATHMM raw prediction score 0.98367 (Tolerated)
SIFT score 0.004 (Deleterious)
LRT score 0.287 (Tolerated)
MutationTaster score 1 (Deleterious)
MutatioinAssessor score 2.355 (Deleterious)
PROVEAN score -3.52 (Deleterious)
MetaSVM score 0.357 (Deleterious)
MetaLR score 0.706 (Deleterious)
MCAP score 0.191 (Deleterious)
FitCons score 0.487 (Highly Significant p < 0.003 )
Genomic Evolutionary Rate Profiling (GERP) score 3.98
PhyloP score based on multiple alignment of 100 vertebrates 7.495
PhastCons score based on multiple alignment of 100 vertebrates 1
SiPhy log transformed odds ratio on multiple alignment of 29 mammals 12.215
Deleterious probability by iFish2 0.9947 (Deleterious)
Deleterious probability by DeFine 0.9264 (Deleterious)
Entrez Gene ID 8647 (NCBI Gene)
Official Gene Symbol ABCB11 (GeneCards)
Number of variants in ABCB11 in this database 3 (view all the variants)
Full name ATP binding cassette subfamily B member 11
Band 2q31.1
Other IDs Vega: OTTHUMG00000154039
OMIM: 603201
HGNC: HGNC:42
Ensembl: ENSG00000073734
Other names BSEP, PGY4, SPGP, ABC16, BRIC2, PFIC2, PFIC-2
Summary The membrane-associated protein encoded by this gene is a member of the superfamily of ATP-binding cassette (ABC) transporters. ABC proteins transport various molecules across extra- and intra-cellular membranes. ABC genes are divided into seven distinct subfamilies (ABC1, MDR/TAP, MRP, ALD, OABP, GCN20, White). This protein is a member of the MDR/TAP subfamily. Members of the MDR/TAP subfamily are involved in multidrug resistance. The protein encoded by this gene is the major canalicular bile salt export pump in man. Mutations in this gene cause a form of progressive familial intrahepatic cholestases which are a group of inherited disorders with severe cholestatic liver disease from early infancy. [provided by RefSeq, Jul 2008]

Individual #1

Individual ID 28867142.26 (view all the variants in this individual)
Pubmed ID 28867142
Whose mosaic mutation Male Patient  
Origin of mosaic mutation in patients de novo
Phenotype 3  
Disease Autism Spectrum Disorders (view all the variants in this disease)
OMIM ID 209850

Publication #1: 28867142

Pubmed ID 28867142
Title Exonic Mosaic Mutations Contribute Risk for Autism Spectrum Disorder
Journal American Journal of Human Genetics
Publication date 2017.08
Disease Autism Spectrum Disorders
Incidence 0.01
Number of cases cases of unknown sex: 247;