Overview

Variant ID 29767
Entrez Gene ID 90268
Gene OTULIN (GeneCards)
Location hg19 5:14693136-14693136
hg38 5:14693027-14693027
Disease Autism Spectrum Disorders (view all the variants in this disease)
Method NextSeq500
Mutation(HGVS format) NC_000005.9:g.14693136 G>T (Genome Assembly: hg19)

Other information

Exon or Intron Exon
Position in protein NA
Amino acid changes in protein NA > NA
Position in cDNA NA
Changes in cDNA NA > NA
mRNA accession NA
mRNA length NA
Reference length 180915260

Annotations and predictions

MAF in gnomAD genome (version 2.0.1) 0
EIGEN score 0.0518
CADD Raw score (version 1.3) 1.207324 (Deleterious)
FATHMM raw prediction score 0.97129 (Tolerated)
Deleterious probability by DeFine 0.8818 (Deleterious)
Entrez Gene ID 90268 (NCBI Gene)
Official Gene Symbol OTULIN (GeneCards)
Number of variants in OTULIN in this database 1 (view all the variants)
Full name OTU deubiquitinase with linear linkage specificity
Band 5p15.2
Other IDs Vega: OTTHUMG00000161762
OMIM: 615712
HGNC: HGNC:25118
Ensembl: ENSG00000154124
Other names GUM, AIPDS, FAM105B
Summary This gene encodes a member of the peptidase C65 family of ubiquitin isopeptidases. Members of this family remove ubiquitin from proteins. The encoded enzyme specifically recognizes and removes M1(Met1)-linked, or linear, ubiquitin chains from protein substrates. Linear ubiquitin chains are known to regulate the NF-kappa B signaling pathway in the context of immunity and inflammation. Mutations in this gene cause a potentially fatal autoinflammatory syndrome in human patients. [provided by RefSeq, Sep 2016]

Individual #1

Individual ID 28867142.34 (view all the variants in this individual)
Pubmed ID 28867142
Whose mosaic mutation Male Patient  
Origin of mosaic mutation in patients de novo
Phenotype 3  
Disease Autism Spectrum Disorders (view all the variants in this disease)
OMIM ID 209850

Publication #1: 28867142

Pubmed ID 28867142
Title Exonic Mosaic Mutations Contribute Risk for Autism Spectrum Disorder
Journal American Journal of Human Genetics
Publication date 2017.08
Disease Autism Spectrum Disorders
Incidence 0.01
Number of cases cases of unknown sex: 247;