Variant ID | 29767 |
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Entrez Gene ID | 90268 |
Gene | OTULIN (GeneCards) |
Location | hg19 5:14693136-14693136
hg38 5:14693027-14693027 |
Disease | Autism Spectrum Disorders (view all the variants in this disease) |
Method | NextSeq500 |
Mutation(HGVS format) | NC_000005.9:g.14693136 G>T (Genome Assembly: hg19) |
Exon or Intron | Exon |
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Position in protein | NA |
Amino acid changes in protein | NA > NA |
Position in cDNA | NA |
Changes in cDNA | NA > NA |
mRNA accession | NA |
mRNA length | NA |
Reference length | 180915260 |
MAF in gnomAD genome (version 2.0.1) | 0 |
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EIGEN score | 0.0518 |
CADD Raw score (version 1.3) | 1.207324 (Deleterious) |
FATHMM raw prediction score | 0.97129 (Tolerated) |
Deleterious probability by DeFine | 0.8818 (Deleterious) |
Entrez Gene ID | 90268 (NCBI Gene) |
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Official Gene Symbol | OTULIN (GeneCards) |
Number of variants in OTULIN in this database | 1 (view all the variants) |
Full name | OTU deubiquitinase with linear linkage specificity |
Band | 5p15.2 |
Other IDs | Vega: OTTHUMG00000161762 OMIM: 615712 HGNC: HGNC:25118 Ensembl: ENSG00000154124 |
Other names | GUM, AIPDS, FAM105B |
Summary | This gene encodes a member of the peptidase C65 family of ubiquitin isopeptidases. Members of this family remove ubiquitin from proteins. The encoded enzyme specifically recognizes and removes M1(Met1)-linked, or linear, ubiquitin chains from protein substrates. Linear ubiquitin chains are known to regulate the NF-kappa B signaling pathway in the context of immunity and inflammation. Mutations in this gene cause a potentially fatal autoinflammatory syndrome in human patients. [provided by RefSeq, Sep 2016] |
Individual ID | 28867142.34 (view all the variants in this individual) |
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Pubmed ID | 28867142 |
Whose mosaic mutation | Male Patient |
Origin of mosaic mutation in patients | de novo |
Phenotype | 3 |
Disease | Autism Spectrum Disorders (view all the variants in this disease) |
OMIM ID | 209850 |
Pubmed ID | 28867142 |
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Title | Exonic Mosaic Mutations Contribute Risk for Autism Spectrum Disorder |
Journal | American Journal of Human Genetics |
Publication date | 2017.08 |
Disease | Autism Spectrum Disorders |
Incidence | 0.01 |
Number of cases | cases of unknown sex: 247; |