Overview

Variant ID 604
Entrez Gene ID 9681
Gene DEPDC5 (GeneCards)
Location hg19 22:32179893-32179893
hg38 22:31783907-31783907
Disease Focal Cortical Dysplasias (view all the variants in this disease)
Method MiSeq
Mutation(HGVS format) NC_000022.10:g.32179893 G>A (Genome Assembly: hg19)

Other information

Exon or Intron Intron
Exon number -1
Position in protein 422
Amino acid changes in protein R > *
Position in cDNA 484
Changes in cDNA G > A
mRNA accession NM_001242896.1
mRNA length 5551
Reference length 51304566

Annotations and predictions

MAF in gnomAD genome (version 2.0.1) 0
EIGEN score 0.7946
CADD Raw score (version 1.3) 6.196342 (Deleterious)
FATHMM raw prediction score 0.97345 (Tolerated)
SIFT score 0.002 (Deleterious)
LRT score 0 (Deleterious)
MutationTaster score 1 (Deleterious)
MutatioinAssessor score 1.82 (Tolerated)
PROVEAN score -2.36 (Tolerated)
MetaSVM score -0.679 (Tolerated)
MetaLR score 0.276 (Tolerated)
MCAP score 0.085 (Deleterious)
FitCons score 0.732 (Highly Significant p < 0.003 )
Genomic Evolutionary Rate Profiling (GERP) score 5.45
PhyloP score based on multiple alignment of 100 vertebrates 8.73
PhastCons score based on multiple alignment of 100 vertebrates 1
SiPhy log transformed odds ratio on multiple alignment of 29 mammals 18.198
Deleterious probability by iFish2 0.8039 (Deleterious)
Deleterious probability by DeFine 0.9424 (Deleterious)
Entrez Gene ID 9681 (NCBI Gene)
Official Gene Symbol DEPDC5 (GeneCards)
Number of variants in DEPDC5 in this database 1 (view all the variants)
Full name DEP domain containing 5
Band 22q12.2-q12.3
Other IDs Vega: OTTHUMG00000030926
OMIM: 614191
HGNC: HGNC:18423
Ensembl: ENSG00000100150
Other names DEP.5, FFEVF, FFEVF1
Summary This gene encodes a member of the IML1 family of proteins involved in G-protein signaling pathways. The mechanistic target of rapamycin complex 1 (mTORC1) pathway regulates cell growth by sensing the availability of nutrients. The protein encoded by this gene is a component of the GATOR1 (GAP activity toward Rags) complex which inhibits the amino acid-sensing branch of the mTORC1 pathway. Mutations in this gene are associated with autosomal dominant familial focal epilepsy with variable foci. A single nucleotide polymorphism in an intron of this gene has been associated with an increased risk of hepatocellular carcinoma in individuals with chronic hepatitis C virus infection. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Mar 2014]

Individual #1

Individual ID 25623524.01 (view all the variants in this individual)
Pubmed ID 25623524
Whose mosaic mutation Female Patient  
Origin of mosaic mutation in patients Paternal
Phenotype 3  
Disease Focal Cortical Dysplasias (view all the variants in this disease)
OMIM ID 607341

Publication #1: 25623524

Pubmed ID 25623524
Title Familial focal epilepsy with focal cortical dysplasia due to DEPDC5 mutations.
Journal Annals of Neurology
Publication date 2015.04
Disease Focal Cortical Dysplasias
Population French
Number of cases Female cases: 2;