Variant ID | 8964 |
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Entrez Gene ID | 2762 |
Gene | GMDS (GeneCards) |
Location | hg19 6:2034471-2034471
hg38 6:2034237-2034237 |
Disease | Asymptomatic |
Method | HiSeq X Ten |
Mutation(HGVS format) | NC_000006.11:g.2034471 T>C (Genome Assembly: GRCh37) |
Exon or Intron | NA |
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Position in protein | NA |
Amino acid changes in protein | NA > NA |
Position in cDNA | NA |
Changes in cDNA | NA > NA |
mRNA accession | NA |
mRNA length | NA |
Reference length | 171115067 |
MAF in gnomAD genome (version 2.0.1) | 0 |
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EIGEN score | -0.3882 |
CADD Raw score (version 1.3) | -0.269719 (Deleterious) |
FATHMM raw prediction score | 0.07187 (Tolerated) |
Deleterious probability by DeFine | 0.3897 (Neutral) |
Entrez Gene ID | 2762 (NCBI Gene) |
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Official Gene Symbol | GMDS (GeneCards) |
Number of variants in GMDS in this database | 8 (view all the variants) |
Full name | GDP-mannose 4,6-dehydratase |
Band | 6p25.3 |
Other IDs | Vega: OTTHUMG00000016143 OMIM: 602884 HGNC: HGNC:4369 Ensembl: ENSG00000112699 |
Other names | GMD, SDR3E1 |
Summary | GDP-mannose 4,6-dehydratase (GMD; EC 4.2.1.47) catalyzes the conversion of GDP-mannose to GDP-4-keto-6-deoxymannose, the first step in the synthesis of GDP-fucose from GDP-mannose, using NADP+ as a cofactor. The second and third steps of the pathway are catalyzed by a single enzyme, GDP-keto-6-deoxymannose 3,5-epimerase, 4-reductase, designated FX in humans (MIM 137020).[supplied by OMIM, Aug 2009] |
Individual ID | 29217584.03 (view all the variants in this individual) |
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Pubmed ID | 29217584 |
Whose mosaic mutation | Normal |
Phenotype | 1 |
Disease | Asymptomatic |
OMIM ID |
Pubmed ID | 29217584 |
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Title | Aging and neurodegeneration are associated with increased mutations in single human neurons. |
Journal | Science |
Publication date | 2018.02 |
Disease | Cockayne syndrome Xeroderma Pigmentosum |
Number of cases | Male cases: 3; Female cases: 6; cases of unknown sex: 15; |